Русский
Early correction of hypospadias in girl with a disorder of sex development. clinical case
DOI: https://dx.doi.org/10.18565/urology.2019.4:91-94
A.V. Anikiev, N.Yu. Kalinchenko, E.A. Volod’ko, D.N. Brovan, A.B. Okulov, O.B. Bezlepkina
1) FGBU National Medical Research Center of Endocrinology of the Ministry of Health of the Russian Federation, Moscow, Russia; 2) Department of Pediatric Surgery of FGBOU DPO «Russian Medical Academy for Postgraduate Education» of the Ministry of Health of the Russian Federation, Moscow, Russia
The presented clinical case of a girl with a salt-wasting form of congenital adrenal hyperplasia in combination with chronic recurrent infection and lower urinary tract dysfunction demonstrates the need to change conventional two-staged approach to surgical feminization in favor of a one-stage intervention in order to prevent a progression of genitourinary complications. After controlling for the underlying condition, the one-stage feminization was performed, including modified tightening introitoplasty using a Passerini-Glazel flap and a correction of hypertrophic clitoris and labia minora. Good short- and long-term results were achieved.
Keywords: hydrocolpos, recurrent urinary tract infection, disorder of sex development, one-stage feminization
About the Autors
Corresponding author: A.V. Anikiev – Ph.D., urologist at the Department of Pediatric Surgery of FGBU National Medical Research Center of Endocrinology of the Ministry of Health of the Russian Federation, Moscow, Russia; e-mail: anikieal70@gmail.com
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