Aim. To analyze the diagnostics results and surgical outcomes in girls with congenital urogenital sinus.
Materials and methods. A total of 9 girls with urogenital sinus were evaluated and treated in the clinical base of the Department of Hospital Pediatric Surgery with a course of oncology at TashPMI during the period from 2009 to 2019.
Results. The results of diagnostics and treatment of 9 patients with various forms of urogenital sinus are presented. In 6 cases the anterior sagittal (transanal) approach was used. The karyotype in 8 girls corresponded to 46,XX, while another girl has karyotype of 46;X0, which is typical for Turner syndrome. Severe degree of virilization was found in 2 patients, which required clitoroplasty.
Conclusion. Traditional methods of surgical correction and modified procedures provide an optimal approach and facilitate the urethral dissection from the vagina with subsequent advancement to the perineum, significantly reducing the indications for the performing a preliminary colostomy.

Keywords: urogenital sinus, children, diagnosis, treatment