Русский
Disorders of sexual differentiation in children: a critical look at open questions (part I)
DOI: https://dx.doi.org/10.18565/urology.2018.2.116-120
N.D. Shiryaev, I.M. Kagantsov, V.V. Sizonov, V.I. Dubrov
Northern State Medical University of Minzdrav of Russia, Arkhangelsk, Russia; Republican Children’s Clinical Hospital, Syktyvkar, Russia; Pitirim Sorokin Syktyvkar State University, Syktyvkar, Russia; RostSMU of Minzdrav of Russia, Rostov-on-Don, Russia; Children’s Hospital #2, Minsk, Republic of Belarus
Management of children with disorders of sexual differentiation (DSD) continues to cause questions and receive criticism. This review discusses some contradictions concerning the newly proposed terminology, nomenclature, and classification. Congenital adrenal hyperplasia (CAH) is the most common cause of DSD, and its management also remains controversial. Therefore, in this part of the article, we critically analyze available literature on gender identity, the need and timing of surgery in children with DSD and 46, XX karyotype.
Keywords: genital surgery in children, gender assignment, congenital adrenal hyperplasia, terminology/nomenclature, disorders of sex development
About the Autors
Corresponding author: I.M. Kagantsov – Dr.Med.Sci., Prof. at the Department of Surgical Diseases, Pitirim Sorokin SSU; Head of the Department of Urology, RCCH, Syktyvkar, Russia; e-mail: ilkagan@rambler.ru
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