Нарушения половой дифференцировки у детей: критический взгляд на нерешенные вопросы (часть I)


DOI: https://dx.doi.org/10.18565/urology.2018.2.116-120

Н.Д. Ширяев, И.М. Каганцов, В.В. Сизонов, В.И. Дубров

ФГБОУ ВО «Северный Государственный медицинский университет» Минздрава России, Архангельск, Россия; ГУ «Республиканская детская клиническая больница», Сыктывкар, Россия; ФГБОУ ВО «Сыктывкарский ГУ им. Питирима Сорокина», Сыктывкар, Россия; ФГБОУ ВО РостГМУ Минздрава России, Ростов-на-Дону, Россия; 2-я детская больница, Минск, Республика Беларусь
Лечение детей с нарушениями половой дифференцировки (НПД) продолжает вызывать вопросы и критику. Ряд противоречий, касающихся вновь предложенных терминологии, номенклатуры и классификации, обсуждается в этом обзоре. Врожденная гиперплазия надпочечников (ВГН) является наиболее частой причиной НПД, и ее лечение также остается противоречивым. Поэтому в этой части статьи мы критически анализируем доступную литературу в отношении назначения пола, необходимости и времени проведения хирургического вмешательства у детей с ВГН и 46,ХХ кариотипом.

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Об авторах / Для корреспонденции


А в т о р д л я с в я з и: И. М. Каганцов – д.м.н., профессор кафедры хирургических болезней ФГБОУ ВО
«СГУ им. Питирима Сорокина», зав. отд. урологии ГУ РДКБ, Сыктывкар, Россия; e-mail: ilkagan@rambler.ru


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